Isselbcher k, braunwald e, wilson j, martin j, fauci. Indice1 resumen2 introduccion3 caso clinico4 discusion. Herlynwerner wunderlich syndrome is a rare congenital anomaly of the urogenital tract, which is characterized by the triad of uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis. Pdf pyometra and pregnancy with herlynwernerwunderlich. Access to society journal content varies across our titles. Anatomically, hwws is characterized by three key anomalies of the female reproductive tract. Wunderlich syndrome unusual complication of spontaneous. Benavides f, albino g, santomil f, verdecchia r vazquezz l, varea s. Herlynwernerwunderlich hww syndrome is a rare congenital disorder in which there is uterus didelphys, obstructed hemivagina and renal agenesis lending its acronym, ohvira syndrome. Jul 15, 2011 the herlynwernerwunderlich syndrome is a rare congenital anomaly characterised by uterus didelphys with blind hemivagina and ipsilateral renal agenesis. Sindrome ohvira hemivagina obstruida y anomalia renal. Angioembolisation revealed the unusual finding of active bleeding from multiple distinct subsegmental renal vessels, for which haemostasis was. Herlynwernerwunderlich syndrome radiology reference.
Spontaneous nontraumatic renal haemorrhage, or wunderlichs syndrome, is a rare but potentially lifethreatening event. Herlynwernerwunderlich syndrome hwws is a rare variant of mullerian duct anomalies. Only a handful of these cases have been associated with pyocolpos. Wunderlich syndrome ws is a rare condition characterized by a nontraumatic spontaneous acute renal hemorrhage into the subcapsular and perirenal spaces, found and described in this case. It may be the first manifestation of a renal angiomyolipoma aml, or rupture of renal artery or intraparenchymal aneurysm. This entity is also known as obstructed hemivagina and ipsilateral renal anomaly ohvira. Wunderlich syndrome is spontaneous, nontraumatic kidney bleeding confined to the subcapsular and perirenal space. It is not to be confused with the wunderlich syndrome. It is most commonly diagnosed in puberty due to pelvic and abdominal pain, but more rarely it can present in neonates or adults, with primary infertility, pyometra, urinary obstruction and. Obstructed hemivagina, didelphys uterus and ipsilateral renal agenesis. Nestor san martin urrutia 2 herlynwernerwunderlich sindrome. Wunderlich syndrome is a rare condition, in which spontaneous nontraumatic renal hemorrhage occurs into the subcapsular and perirenal spaces 2.
Utero didelfo con hemivagina ciega y agenesia renal homolateral. If you have access to a journal via a society or association membership, please browse to your society journal, select an article to view, and follow the instructions in this box. Tickoo, anuradha gopalan, pathologic features of renal cortical tumors, urol clin n am 35 2008 551561 links 11. Spontaneous nontraumatic renal haemorrhage, or wunderlich s syndrome, is a rare but potentially lifethreatening event. The herlynwerner wunderlich syndrome is a rare congenital anomaly characterised by uterus didelphys with blind hemivagina and ipsilateral renal agenesis. Herlynwerner wunderlich hww syndrome is a rare congenital disorder in which there is uterus didelphys, obstructed hemivagina and renal agenesis lending its acronym, ohvira syndrome. Obstructed hemivagina and ipsilateral renal anomaly ohvira, also known as herlynwernerwunderlich syndrome, is a rare syndrome with only a few hundred reported cases described since 1922. Clinical presentation wunderlich syndrome is clinically characterized by lenks triad. Herlynwernerwunderlich hww syndrome, is a rare anomaly characterized by mullerian duct anomalies mda associated with mesonephric duct anomalies 3. Wunderlich syndrome a rare cause of acute abdomen in patients with acquired. We present the case of a 63yearold man on clopidogrel who became haemodynamically unstable as a result of this condition. It usually presents after menarche with progressive pelvic pain during menses secondary to haematocolpos.